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fatale postvirale neurodegeneratieve aandoening (aandoening)
fatale postvirale neurodegeneratieve aandoening
Fatal post-viral neurodegenerative disorder
A rare neuroinflammatory disease characterized by the onset of ataxia, dysarthria and cerebral white matter changes that are triggered by viral infection. Episodic progressive neurodegeneration (manifesting with loss of motor and verbal skills, muscle weakness, further cerebral white matter degeneration and eventually, death) is observed in the absence of hematopathology, cytokine overproduction, fever, hypertriglyceridemia, hypofibrinogenemia and hyperferritinemia.
Id774206008
StatusPrimitive
Associated morphologydegeneratieve afwijking
Finding sitestructuur van encephalon
Associated morphologyinflammatoire morfologie
Finding sitestructuur van encephalon
Clinical courseprogressief
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetG04.8
TermOverige gespecificeerde encefalitis, myelitis en encefalomyelitis
SNOMED CT to Orphanet simple map391343
SNOMED CT to ICD-10 extended map
TargetG04.8
RuleTRUE
AdviceALWAYS G04.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified