| syndroom van pyogene artritis, pyoderma gangraenosum en acne (aandoening) | | syndroom van pyogene artritis, pyoderma gangraenosum en acne | | PAPA-syndroom
|  | Dit betekent dat je ontstoken gewrichten, zweren op je huid en puistjes hebt. Onder je huid heb je holtes die zijn gevuld met vocht. Dit komt omdat je afweersysteem je eigen lichaam aanvalt. | | Pyogenic arthritis, pyoderma gangrenosum, acne syndrome | | PAPA syndrome
PAPA (pyogenic arthritis, pyoderma gangrenosum, acne) syndrome
Familial recurrent arthritis
| | Pyogenic arthritis-pyoderma gangrenosum-acne syndrome is a rare pleiotropic autoinflammatory disorder of childhood, primarily affecting the joints and skin. |
| | Id | 724015007 | | Status | Primitive |
| DHD Diagnosis thesaurus reference set |
| SNOMED CT to Orphanet simple map | 69126 |
| SNOMED CT to ICD-10 extended map | | Target | D89.8 | | Rule | TRUE | | Advice | ALWAYS D89.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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