syndroom van odontomen en dysfagie (aandoening) | | syndroom van odontomen en dysfagie | | syndroom van Boder syndroom van odontomatose en stenose van aorta en oesofagus syndroom van Bader
| | Boder syndrome | | Odontoma dysphagia syndrome
| | Odontoma-dysphagia syndrome is a malformation syndrome, characterized by odontomas (undifferentiated mass of the esophagus) and severe dysphagia. |
| Id | 716180009 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | Target | Q87.8 | Term | Overige gespecificeerde congenitale gestoorde-ontwikkelingssyndromen, niet elders geclassificeerd |
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SNOMED CT to Orphanet simple map | 2724 |
SNOMED CT to ICD-10 extended map | Target | D16.5 | Rule | TRUE | Advice | ALWAYS D16.5 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | Correlation | SNOMED CT source code to target map code correlation not specified |
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