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hereditair angio-oedeem type III (aandoening)
hereditair angio-oedeem type III
Hereditary angioedema with normal C1 esterase inhibitor activity
Hereditary angioedema - type 3
Hereditary angioneurotic edema with normal C1 esterase inhibitor activity
Hereditary angioedema without abnormal C1 inhibitor levels or function. One type has been found mostly in females in which symptoms may be triggered by pregnancy or estrogen-containing oral contraceptives. Mechanisms include mutations of the genes encoding coagulation factor XII, angiopoietin-1, plasminogen and as yet undefined factors.
Id427167008
StatusPrimitive
Associated morphologyangio-oedeem
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD84.1
TermStoornissen in complementsysteem
SNOMED CT to Orphanet simple map528647
SNOMED CT to ICD-10 extended map
TargetD84.1
RuleTRUE
AdviceALWAYS D84.1
CorrelationSNOMED CT source code to target map code correlation not specified