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hereditair angio-oedeem (aandoening)
hereditair angio-oedeem
Dit betekent dat je huid of slijmvliezen opzwellen. Dat komt door een probleem met je bloedvaten. Je bent met dit probleem geboren.
Hereditary angioedema
Hereditary Quincke's edema
Hereditary angioneurotic edema
HAE - Hereditary angioedema
HANE - Hereditary angioneurotic edema
Hereditary angioedema (HAE) is a genetic disease characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain.
Id82966003
StatusDefined
Associated morphologyangio-oedeem
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD84.1
TermStoornissen in complementsysteem
SNOMED CT to Orphanet simple map91378
SNOMED CT to MedDRA simple map10019860
SNOMED CT to ICD-10 extended map
TargetD84.1
RuleTRUE
AdviceALWAYS D84.1
CorrelationSNOMED CT source code to target map code correlation not specified
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