angio-oedeem door stoornis van kininemetabolisme	autosomaal dominante hereditaire aandoening	defect van complementregulerende factor	hereditair angio-oedeem met deficiëntie van C1-esteraseremmer	hereditaire aandoening van immuunsysteem
\|	\|	\|	\|	\|

hereditair angio-oedeem type I (aandoening)
	hereditair angio-oedeem type I
	Hereditary C1 esterase inhibitor deficiency - deficient factor
	Hereditary angioedema - type 1 Hereditary angioneurotic edema - type 1 C1 esterase inhibitor deficiency - type 1

Id	234619000
Status	Primitive

Finding site	structuur van immuunsysteem
Pathological process	afwijkend immuunproces

Associated morphology	angio-oedeem
Causative agent	Kallidin I

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	D84.1
Term	Stoornissen in complementsysteem

SNOMED CT to Orphanet simple map

100050

SNOMED CT to ICD-10 extended map

Target	D84.1
Rule	TRUE
Advice	ALWAYS D84.1
Correlation	SNOMED CT source code to target map code correlation not specified