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niet-amyloïde monoklonale immuunglobulinestapelingsziekte (aandoening)
niet-amyloïde monoklonale immuunglobulinestapelingsziekte
niet-amyloïde MIDD
niet-amyloïde 'monoclonal immunoglobulin deposition disease'
Non-amyloid monoclonal immunoglobulin deposition disease
Non-amyloid MIDD (monoclonal immunoglobulin deposition disease)
Randall disease
A rare secondary glomerular disease characterized by proteinuria, dysproteinemia, nephrotic syndrome, and nodular glomerulopathy leading to renal failure, with or without extra-renal manifestations. The renal biopsy shows typical deposits of monoclonal immunoglobulins that do not show a fibrillar organization and are negative for Congo red staining. Associated signs and symptoms depend on the involvement of other organs, liver, heart, nerve fibers, gastrointestinal tract or skin.
Id829971006
StatusPrimitive
Associated morphologyimmuunglobulinestapelingsziekte
Finding sitestructuur van glomerulus
Pathological processafwijkend immuunproces
Has interpretationaangetoond
InterpretsParaprotein measurement
SNOMED CT to Orphanet simple map86861
SNOMED CT to ICD-10 extended map
TargetD89.8
RuleTRUE
AdviceALWAYS D89.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified
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