| hooggradig neuro-endocrien carcinoom van corpus uteri (aandoening) | | hooggradig neuro-endocrien carcinoom van corpus uteri | | hooggradig NEC van corpus uteri
slecht gedifferentieerd neuro-endocrien neoplasma van corpus uteri
| | High-grade neuroendocrine carcinoma of corpus uteri | | Poorly differentiated neuroendocrine carcinoma of corpus uteri
| | An extremely rare aggressive primary uterine neoplasm, originating from neuroendocrine cells scattered within the endometrium. Macroscopic characteristics are a bulky frequently polypoid mass with abundant necrosis located in the uterus. Histological characteristics are rosette-like and cord-like structures consisting of small rounded cells with oval nuclei and scarce cytoplasm. Patients often present with dysfunctional uterine bleeding, pelvic or abdominal mass and abdominal pain, especially in later stages of the disease. Symptomatic metastatic spread or symptoms related to a paraneoplastic syndrome such as retinopathy or Cushing syndrome due to ectopic ACTH production may be associated. |
| | DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | C54.9 | | Term | Maligne neoplasma van corpus uteri, niet gespecificeerd |
|
| SNOMED CT to Orphanet simple map | 213731 |
| SNOMED CT to ICD-10 extended map | | Target | C54.9 | | Rule | TRUE | | Advice | ALWAYS C54.9 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
|
|
