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rabdomyosarcoom van vulva en vagina (aandoening)
rabdomyosarcoom van vulva en vagina
vulvovaginaal rabdomyosarcoom
Vulvovaginal rhabdomyosarcoma
Rhabdomyosarcoma of vulva and vagina
A rare vulvovaginal neoplasm, a highly malignant soft tissue sarcoma composed of cells with round to oval or spindle-shaped nuclei and eosinophilic cytoplasm that may show differentiation towards striated muscle cells. It usually affects children and presents with a vulvar or vaginal mass that may be polypoid or grape-like (embryonal subtype) and associated with bleeding and ulceration.
Id766759009
StatusDefined
Associated morphologyrabdomyosarcoom
Finding sitestructuur van vagina
Associated morphologyrabdomyosarcoom
Finding sitestructuur van vulva
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetC52
TermMaligne neoplasma van vagina
TargetC51.9
TermMaligne neoplasma van vulva, niet gespecificeerd
SNOMED CT to Orphanet simple map206492
SNOMED CT to ICD-10 extended map
TargetC52
RuleTRUE
AdviceALWAYS C52 | MAPPED FOLLOWING WHO GUIDANCE | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified
TargetC51.9
RuleTRUE
AdviceALWAYS C51.9 | MAPPED FOLLOWING WHO GUIDANCE | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified