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syndroom van arteriƫle dissectie en lentiginose (aandoening)
syndroom van arteriƫle dissectie en lentiginose
Arterial dissection and lentiginosis syndrome
A rare association syndrome, reported in several members of two families to date with characteristics of arterial dissection, occurring at an early age and presenting with a range of manifestations depending on the vascular territory involved, in association with cystic medial necrosis and multiple lentigines.
Id720512007
StatusPrimitive
Associated morphologydissectie
Finding sitestructuur van wand van arterie
Occurrencecongenitaal
Pathological processproces van pathologische ontwikkeling
Associated morphologylentigo
Finding sitestructuur van huid
Occurrencecongenitaal
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetQ87.8
TermOverige gespecificeerde congenitale gestoorde-ontwikkelingssyndromen, niet elders geclassificeerd
SNOMED CT to Orphanet simple map1682
SNOMED CT to ICD-10 extended map
TargetQ87.8
RuleTRUE
AdviceALWAYS Q87.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified