| leiomyomateus neoplasma van orbitaal vasculair glad spierweefsel (aandoening) | | leiomyomateus neoplasma van orbitaal vasculair glad spierweefsel | | Orbital leiomyoma | | Leiomyoma of orbit
| | Orbital leiomyoma is a rare benign smooth muscle tumor arising from the walls of orbital vessels characterized by its slow growth and well encapsulated nature. It is usually located in an extraconal position, commonly manifesting with painless proptosis. The tumor is composed of spindle cells arranged in a fibrous stroma rich in dilated sinusoidal capillaries. The nuclei of tumor cells are oval with blunted ends and there are no mitotic figures. Orbital leiomyoma when excised has excellent prognosis for vision and life. One case of orbital leiomyosarcoma that possibly represents sarcomatous change in an orbital leiomyoma following radiation treatment has been reported. |
| | DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | D31.6 | | Term | Benigne neoplasma van orbita, niet gespecificeerd |
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| SNOMED CT to Orphanet simple map | 52994 |
| SNOMED CT to ICD-10 extended map | | Target | D31.6 | | Rule | TRUE | | Advice | ALWAYS D31.6 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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