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Periodic fever and aphthous stomatitis with pharyngitis and cervical lymphadenitis syndrome (disorder)
PFAPA syndrome
Marshall syndrome with periodic fever
Periodic fever and aphthous stomatitis with pharyngitis and cervical lymphadenitis syndrome
An auto inflammatory syndrome with characteristics of recurrent febrile episodes associated with aphthous stomatitis, pharyngitis and cervical adenitis. Usually presents during early childhood with recurrent episodes of fever during which children appear very ill. Aphthous stomatitis presents with relatively painless small, round and shallow lesions on the tongue and oral mucosa that recover completely in 10-14 days. Most patients present with tonsillitis, occasionally with white exudates and a general pharyngitis. Episodes recur every 3-5 weeks, often in a predictable fashion with patients describing a mild malaise the day before recurrence. An idiopathic inflammatory condition.
Id717231003
StatusPrimitive
Associated morphologyinflammatoire morfologie
Finding sitestructuur van pharynx
Associated morphologyaft
Finding sitestructuur van tunica mucosa oris
Has interpretationboven referentiebereik
Interpretslichaamstemperatuur
DHD Diagnosethesaurus-referentieset
referentieset met complexe 'mapping' naar ICD-10
TargetE85.0
RuleTRUE
AdviceALWAYS E85.0
CorrelationSNOMED CT source code to target map code correlation not specified
TargetI88.9
RuleTRUE
AdviceALWAYS I88.9
CorrelationSNOMED CT source code to target map code correlation not specified
TargetK12.0
RuleTRUE
AdviceALWAYS K12.0
CorrelationSNOMED CT source code to target map code correlation not specified
TargetJ02.9
RuleTRUE
AdviceALWAYS J02.9
CorrelationSNOMED CT source code to target map code correlation not specified