primaire biliaire cholangitis
progressieve systemische sclerose
systemische sclerose met gelimiteerde betrokkenheid van huid
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primaire levercirrose gelijktijdig met systemische sclerodermie (aandoening)
primaire levercirrose gelijktijdig met systemische sclerodermie
primaire biliaire cirrose gelijktijdig met systemische sclerodermie
syndroom van Reynolds
primaire biliaire cirrose gelijktijdig met systemische sclerose
Reynolds syndrome
Primary biliary cirrhosis co-occurrent with systemic scleroderma
An autoimmune disorder characterized by the association of primary biliary cirrhosis with limited cutaneous systemic sclerosis. Onset occurs between 30-65 years. Occurs sporadically, but rare familial cases with an unknown inheritance pattern have been observed. There is no cure and management is mainly supportive.
Id715401008
StatusDefined
Clinical courseprogressief
Associated morphologyfibrose
Finding sitestructuur van bindweefsel
Pathological processauto-immuunproces
Associated morphologychronische fibrose
Finding siteStructure of intrahepatic bile duct
Pathological processauto-immuunproces
Associated morphologynodulaire regeneratie
Finding siteStructure of intrahepatic bile duct
Pathological processauto-immuunproces
Associated morphologyinflammatoire morfologie
Finding siteStructure of intrahepatic bile duct
Pathological processauto-immuunproces
Pathological processproces van overgevoeligheid
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetK74.3
TermPrimaire biliaire cirrose
TargetM34.9
TermSystemische sclerose, niet gespecificeerd
SNOMED CT to Orphanet simple map779
SNOMED CT to ICD-10 extended map
TargetK74.3
RuleTRUE
AdviceALWAYS K74.3
CorrelationSNOMED CT source code to target map code correlation not specified
TargetM34.9
RuleTRUE
AdviceALWAYS M34.9
CorrelationSNOMED CT source code to target map code correlation not specified