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familiair sacculair cerebraal aneurysma (aandoening)
familiair sacculair cerebraal aneurysma
familiair sacculair hersenaneurysma
Familial cerebral saccular aneurysm
Familial intracranial saccular aneurysm
Familial berry aneurysm
A rare genetic neurovascular malformation characterized by sac-like bulging of cerebral arteries due to weakening of the endothelial layer. Familial occurrence is suspected when two or more affected first- to third-degree relatives are present in a family. Aneurysms may remain asymptomatic throughout life, or rupture and thereby cause potentially life-threatening subarachnoid hemorrhage. Patients with familial cerebral saccular aneurysm are more likely to develop more than one brain aneurysm, are at greater risk of rupture, and tend to have poorer outcome after rupture than patients with sporadic cerebral aneurysms.
Id703226008
StatusPrimitive
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetI67.1
TermCerebraal aneurysma zonder ruptuur
SNOMED CT to Orphanet simple map231160
SNOMED CT to ICD-10 extended map
TargetI67.1
RuleTRUE
AdviceALWAYS I67.1
CorrelationSNOMED CT source code to target map code correlation not specified