autosomaal recessieve hereditaire aandoening	familiaire aandoening	hereditaire aandoening van cardiovasculair systeem	pulmonaire capillaire hemangiomatose
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familiaire pulmonale capillaire hemangiomatose (aandoening)
	familiaire pulmonale capillaire hemangiomatose
	familiale pulmonale capillaire hemangiomatose familiaire pulmonaire capillaire hemangiomatose
	Familial pulmonary capillary hemangiomatosis
	An autosomal recessive subtype of primary pulmonary hypertension which has histological characteristics of widespread fibrous intimal proliferation of septal veins and preseptal venules. There is frequent association with pulmonary capillary dilatation and proliferation and the disease can cause occult alveolar hemorrhage.

Id	234161007
Status	Defined

Associated morphology	hemangiomatose
Finding site	structuur van capillair van long

SNOMED CT to ICD-10 extended map

Target	D18.0
Rule	TRUE
Advice	ALWAYS D18.0 \| POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
Correlation	SNOMED CT source code to target map code correlation not specified