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familiaire pulmonale capillaire hemangiomatose (aandoening)
familiaire pulmonale capillaire hemangiomatose
familiaire pulmonaire capillaire hemangiomatose
familiale pulmonale capillaire hemangiomatose
Familial pulmonary capillary hemangiomatosis
An autosomal recessive subtype of primary pulmonary hypertension which has histological characteristics of widespread fibrous intimal proliferation of septal veins and preseptal venules. There is frequent association with pulmonary capillary dilatation and proliferation and the disease can cause occult alveolar hemorrhage.
Id234161007
StatusPrimitive
Associated morphologyhemangiomatose
Finding sitestructuur van vas capillare
referentieset met complexe 'mapping' naar ICD-10
TargetD18.0
RuleTRUE
AdviceALWAYS D18.0 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified