| A rare cerebellar ataxia characterized by cerebellar inflammation caused by viral or bacterial infection-triggered, immune-mediated mechanisms. It mainly affects young children following an episode of usually viral infection (notably varicella), but sometimes also adults, mostly upon Epstein-Barr virus or mycoplasma infection. Affected individuals mainly present with acute-onset afebrile gait ataxia, meningeal signs, high intracranial pressure with or without extracerebellar manifestations (such as clouding of consciousness, seizures and altered mental status) or extracerebellar focal signs. Mild behavioral changes can also be present. Pleocytosis in cerebrospinal fluid is reported in the majority of the patients. |
