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syndroom van pyoderma gangraenosum, acne, hidradenitis suppurativa en spondylitis ankylopoetica (aandoening)
syndroom van pyoderma gangraenosum, acne, hidradenitis suppurativa en spondylitis ankylopoetica
PASS-syndroom
PASS syndrome
Pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis syndrome
PASS (pyoderma gangrenosum, acne, hidradenitis suppurativa, ankylosing spondylitis) syndrome
A rare autoinflammatory syndrome with characteristics of a chronic-relapsing course of the combination of pyoderma gangrenosum, acne, hidradenitis suppurativa (which, in addition to axillae and inguinal folds, can be observed on upper and lower limbs, back, and buttocks, among others), and ankylosing spondylitis. Typical age of onset is adolescence to young adulthood, with the different signs and symptoms appearing simultaneously or subsequently.
Id1336115002
StatusPrimitive
Clinical coursebeloop met terugval
Associated morphologyneutrofiele infiltratie
Finding sitestructuur van huid
Associated morphologyinflammatoire morfologie
Finding sitestructuur van immuunsysteem
Pathological processafwijkend immuunproces
SNOMED CT to ICD-10 extended map
TargetL88
RuleTRUE
AdviceALWAYS L88 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified