acne
auto-inflammatoire aandoening
chronische aandoening van immuunfunctie
chronische artropathie
chronische dermatitis
chronische infectieuze aandoening
chronische ziekte van immuunsysteem
genetische aandoening
hidradenitis suppurativa met pyoderma gangraenosum
pyogene artritis
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syndroom van pyogene artritis, pyoderma gangraenosum, acne en hidradenitis suppurativa (aandoening)
syndroom van pyogene artritis, pyoderma gangraenosum, acne en hidradenitis suppurativa
PAPASH-syndroom
PAPASH syndrome
Pyogenic arthritis, pyoderma gangrenosum, acne, hidradenitis suppurativa syndrome
PAPASH (pyogenic arthritis, pyoderma gangrenosum, acne, hidradenitis suppurativa) syndrome
A rare autoinflammatory syndrome with characteristics of a chronic-relapsing course of the combination of pyogenic arthritis, pyoderma gangrenosum, acne, and hidradenitis suppurativa (which, in addition to axillae and inguinal folds, can be observed on the face, neck, scalp, back, and buttocks, among others). Typical age of onset is adolescence to young adulthood, with the different signs and symptoms appearing simultaneously or subsequently.
Id1336114003
StatusPrimitive
Clinical coursebeloop met terugval
Associated morphologyneutrofiele infiltratie
Finding sitestructuur van huid
Associated morphologychronische purulente ontsteking
Causative agentdomein Bacteria
Finding sitestructuur van huid met apocriene zweetklier
Pathological processinfectieus proces
Associated morphologyinflammatoire morfologie
Finding sitestructuur van immuunsysteem
Pathological processafwijkend immuunproces
Associated morphologypurulente ontsteking
Finding sitestructuur van gewricht
Pathological processinfectieus proces
Associated morphologyafwijkend weefsel
Finding sitecomplex van haar, haarfollikel, musculus arrector pili en talgklier
SNOMED CT to ICD-10 extended map
TargetL88
RuleTRUE
AdviceALWAYS L88 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified