| familiair gigantiform cementoom van kaak (aandoening) | | familiair gigantiform cementoom van kaak | | familiaal ossificerend fibroom van kaak
familiair cementoma gigantiforme van kaak
familiale floride cemento-osseuze dysplasie van kaak
| | Familial gigantiform cementoma of jaw | | Familial ossifying fibroma of jaw
Multiple ossifying fibroma of jaw
| | A rare genetic bone disease with characteristics of multifocal, painless, benign fibro-cemento-osseous lesions of the jaw which expand progressively and can cause severe facial deformity. It usually manifests at an early age and is often associated with abnormalities of the long bones and pathologic fractures. Radiologically, the lesions are of mixed radiopaque/radiolucent appearance. Incomplete surgical removal may lead to more rapid growth of the residual lesion. |
| | Id | 1263445009 | | Status | Primitive |
| SNOMED CT to Orphanet simple map | 435329 |
| SNOMED CT to ICD-10 extended map | | Target | D16.4 | | Rule | TRUE | | Advice | ALWAYS D16.4 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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