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congenitale systemische arterioveneuze fistel (aandoening)
congenitale systemische arterioveneuze fistel
aangeboren AVF in systemische circulatie
Congenital systemic arteriovenous fistula
A rare potentially life-threatening vascular malformation with characteristics of a direct communication between an artery and a vein, without the interposition of the capillary bed, occurring in the systemic circulation (mainly the cranium, liver, lungs, extremities, and vessels in or near the thoracic wall). Manifestations are variable depending on size and extent of the fistula, the involved blood vessels and the precise location of the collaterals and may include systolic or continuous murmur over the affected organ, tachycardia, increased stroke volume, cardiomegaly and increased pulmonary vascular markings.
Id786041005
StatusPrimitive
Associated morphologyarterioveneuze fistel
Finding siteregionale vaatstructuur
Occurrencecongenitaal
Pathological processproces van pathologische ontwikkeling
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetQ27.3
TermPerifere arterioveneuze misvorming
SNOMED CT to Orphanet simple map2039
SNOMED CT to ICD-10 extended map
TargetQ27.3
RuleTRUE
AdviceALWAYS Q27.3
CorrelationSNOMED CT source code to target map code correlation not specified