communicerende hydrocefalie	congenitale afwijking van meningen	congenitale hydrocefalie	malformatiesyndroom met betrokkenheid van meerdere systemen	mega cisterna magna	naevus flammeus	structurele afwijking van subarachnoïdale ruimte
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syndroom van naevus flammeus, mega cisterna magna en hydrocefalie (aandoening)
	syndroom van naevus flammeus, mega cisterna magna en hydrocefalie
	syndroom van naevus flammeus, mega cisterna magna en hydrocephalus Nova-syndroom
	Port-wine nevi, mega cisterna magna, hydrocephalus syndrome
	Nova syndrome
	A rare developmental defect during embryogenesis syndrome characterized by a glabellar capillary malformation, congenital communicating hydrocephalus, and posterior fossa brain abnormalities, including Dandy-Walker malformation, cerebellar vermis agenesis, and mega cisterna magna. Seizures are occasionally associated. There have been no further descriptions in the literature since 1979.

Id	783701002
Status	Primitive

Associated morphology	morfologische afwijking
Finding site	structuur van capillair van huid
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

Associated morphology	dilatatie
Finding site	structuur van liquorcirculatie in hersenen
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

Associated morphology	vergroting
Finding site	gehele cisterna cerebellomedullaris posterior
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	Q87.8
Term	Overige gespecificeerde congenitale gestoorde-ontwikkelingssyndromen, niet elders geclassificeerd

SNOMED CT to Orphanet simple map

2703

SNOMED CT to ICD-10 extended map

Target	Q03.8
Rule	TRUE
Advice	ALWAYS Q03.8 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified