aneurysma van arterie	idiopathische neuritis optica	idiopathische retinitis	neuroretinitis	retinale vasculitis
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syndroom van idiopathische retinale vasculitis, aneurysmata en neuroretinitis (aandoening)
	syndroom van idiopathische retinale vasculitis, aneurysmata en neuroretinitis
	IRVAN-syndroom
	IRVAN syndrome
	Idiopathic retinal vasculitis, aneurysms, neuroretinitis syndrome IRVAN (idiopathic retinal vasculitis, aneurysms, neuroretinitis) syndrome
	A rare retinal vasculopathy disease characterized by idiopathic retinal vasculitis (IRV), aneurysmal dilations (A) at arteriolar bifurcations, and neuroretinitis (N), which if untreated progresses to peripheral capillary non-perfusion, retinal neovascularization, and macular exudation, leading to severe, bilateral vision loss.

Id	783090002
Status	Primitive

Associated morphology	inflammatoire morfologie
Finding site	structuur van papilla nervi optici

Associated morphology	aneurysma
Finding site	arterie

Associated morphology	inflammatoire morfologie
Finding site	structuur van bloedvat van retina

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	H35.0
Term	'Background' retinopathie en vasculaire veranderingen van retina

SNOMED CT to Orphanet simple map

209943

SNOMED CT to ICD-10 extended map

Target	H35.0
Rule	TRUE
Advice	ALWAYS H35.0 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified