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verworven hemofagocytaire lymfohistiocytose bij maligne neoplasma (aandoening)
verworven hemofagocytaire lymfohistiocytose bij maligne neoplasma
Acquired hemophagocytic lymphohistiocytosis associated with malignant disease
A rare secondary hemophagocytic lymphohistiocytosis characterized by occurring as either initial presentation of a malignant disease or at any stage during chemotherapy. The common associated malignancies are leukemias, B-cell, T-cell or NK-cell lymphomas, and Hodgkin lymphoma. Typical clinical manifestation includes fever, hepatosplenomegaly and cytopenias, combined with specific laboratory findings.
Id782915004
StatusDefined
Associated morphologymaligne neoplasma
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD76.1
TermHemofagocytaire lymfohistiocytose
SNOMED CT to Orphanet simple map158057
SNOMED CT to ICD-10 extended map
TargetD76.1
RuleTRUE
AdviceALWAYS D76.1 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified