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neonatale sclerodermie (aandoening)
neonatale sclerodermie
systemische sclerose bij neonaat
sclerodermie bij pasgeborene
Neonatal scleroderma
A rare secondary neonatal autoimmune disease characterized by neonatal onset of erythematous skin lesions with a linear appearance that gradually become indurated and hyperpigmented and progressively present skin atrophy. Positive serum antibodies (in particular antinuclear antibodies and/or rheumatoid factor) may be associated.
Id774080007
StatusPrimitive
Associated morphologyerytheem
Finding sitestructuur van huid
Occurrenceneonataal
Pathological processauto-immuunproces
Finding sitestructuur van bindweefsel
Occurrenceneonataal
Pathological processauto-immuunproces
DHD Diagnosis thesaurus reference set
SNOMED CT to Orphanet simple map398127
SNOMED CT to ICD-10 extended map
TargetP83.8
RuleTRUE
AdviceALWAYS P83.8
CorrelationSNOMED CT source code to target map code correlation not specified