| syndroom van verrukeuze epidermale naevus, angiodysplasie en aneurysma (aandoening) | | syndroom van verrukeuze epidermale naevus, angiodysplasie en aneurysma | | syndroom van naevus verrucosus, angiodysplasie en aneurysma
| | NEVADA syndrome | | Nevus epidermicus verrucosus with angiodysplasia and aneurysm syndrome
NEVADA (nevus epidermicus verrucosus with angiodysplasia and aneurysm) syndrome
| | A rare life-threatening cutaneous disease characterized by a keratinocytic epidermal nevus presenting thick, hystrix-like, white or brownish hyperkeratosis associated with multiple extracutaneous vascular malformations, including angiodysplasia that involves large-vessel arteriovenous shunts that may be fatal during the neonatal period. |
| | Id | 773986009 | | Status | Primitive |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | Q84.8 | | Term | Overige gespecificeerde congenitale misvormingen van huidadnexen |
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| SNOMED CT to Orphanet simple map | 370059 |
| SNOMED CT to ICD-10 extended map | | Target | Q84.8 | | Rule | TRUE | | Advice | ALWAYS Q84.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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