|||||
pemphigus herpetiformis (aandoening)
pemphigus herpetiformis
herpetiforme pemfigus
Herpetiform pemphigus
A rare superficial pemphigus disease characterized by severe intractable pruritus with erythematous or urticarial plaques and vesicles organized in a herpetiform pattern. Mucosae are generally spared. Eosinophilia in peripheral blood and low titers of circulating autoantibodies are observed in many cases. Histologically, minimal or no apparent acantholysis is associated.
Id771145006
StatusPrimitive
Associated morphologybulla
Causative agentAutoantibody
Finding sitestructuur van huid
Pathological processauto-immuunproces
Associated morphologyacantholyse
Causative agentAutoantibody
Finding sitestructuur van huid
Pathological processauto-immuunproces
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetL10.8
TermOverige gespecificeerde vormen van pemphigus
SNOMED CT to Orphanet simple map208524
SNOMED CT to ICD-10 extended map
TargetL10.8
RuleTRUE
AdviceALWAYS L10.8
CorrelationSNOMED CT source code to target map code correlation not specified