chronische ziekte van gebitselement en/of ondersteunende structuur	dentinedysplasie	osteosclerose
\|	\|	\|

syndroom van dentinedysplasie en osteosclerose (aandoening)
	syndroom van dentinedysplasie en osteosclerose
	Dentin dysplasia with sclerotic bone syndrome
	Dentin dysplasia, sclerotic bones syndrome
	A rare genetic odontologic disease with characteristics of the clinical, radiographic and histologic features of dentin dysplasia and osteosclerosis of all long bones, with heavy cortical bone and narrowed or occluded marrow spaces. There have been no further descriptions in the literature since 1977.

Id	770943008
Status	Primitive

Associated morphology	osteosclerose
Finding site	botstructuur
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

Associated morphology	dysplasie
Finding site	structuur van dentine
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

Clinical course

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	K00.5
Term	Erfelijke afwijkingen van tandstructuur, niet elders geclassificeerd

Target	Q77.4
Term	Achondroplasie

SNOMED CT to Orphanet simple map

99792

SNOMED CT to ICD-10 extended map

Target	K00.5
Rule	TRUE
Advice	ALWAYS K00.5
Correlation	SNOMED CT source code to target map code correlation not specified

Target	Q77.4
Rule	TRUE
Advice	ALWAYS Q77.4
Correlation	SNOMED CT source code to target map code correlation not specified