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mesiale temporalekwabepilepsie met sclerose van hippocampus (aandoening)
mesiale temporalekwabepilepsie met sclerose van hippocampus
mesiale temporale epilepsie met hippocampale sclerose
Mesial temporal lobe epilepsy with hippocampal sclerosis
MTLE-HS - mesial temporal lobe epilepsy with hippocampal sclerosis
A rare epilepsy syndrome defined by seizures originating in limbic areas of the mesial temporal lobe, particularly in the hippocampus, amygdala, and in the parahippocampal gyrus and its connections, and hippocampal sclerosis, usually unilateral or asymmetric. It is frequently associated with an initial precipitating event, such as febrile seizures, hypoxia, intracranial infection or head trauma, most often occurring in the first five years of life, followed by a latent period without seizures. Typical seizures consist of a characteristic aura that is frequently a rising epigastric sensation associated with emotional disturbances, illusions, and autonomic symptoms (widened pupils, palpitations), progressive impairment of consciousness, oro-alimentary automatisms (lip smacking, chewing, licking, tooth grinding), behavioral arrest, head deviation, dystonic postures, hand and verbal automatisms. Seizures are followed by postictal dysfunction. Initially, seizures are easily controlled with antiepileptic drugs, later they frequently become refractory and associated with progressive behavioral changes and memory deficits.
Id770643005
StatusPrimitive
Associated morphologysclerose
Finding sitestructuur van hippocampus
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetG40.2
TermLokalisatiegebonden (focale)(partiƫle) symptomatische epilepsie en epileptische syndromen met complexe partiƫle aanvallen
SNOMED CT to Orphanet simple map99701
SNOMED CT to ICD-10 extended map
TargetG40.2
RuleTRUE
AdviceALWAYS G40.2 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified