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intraneuraal perineurioom (aandoening)
intraneuraal perineurioom
Intraneural perineurioma
Intraneural perineurioma is a rare tumor of cranial and spinal nerves arising from peripheral nerve sheath and composed exclusively or predominantly of cells showing perineurial differentiation. It presents as a localized, tubular or fusiform enlargement of a nerve or nerve segment, usually in the extremities or the trunk, associated with a motor-predominant mononeuropathy including slow, painless, gradual loss of motor function in the involved nerve trunk with muscle weakness and atrophy and, rarely, sensory dysfunction. Cranial nerve involvement is rare.
Id768934004
StatusDefined
DHD Diagnosis thesaurus reference set
SNOMED CT to Orphanet simple map100003
SNOMED CT to ICD-10 extended map
TargetD36.1
RuleTRUE
AdviceALWAYS D36.1 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified