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'pure red cell aplasia' bij volwassene (aandoening)
'pure red cell aplasia' bij volwassene
PRCA op volwassen leeftijd
Adult pure red cell aplasia
A rare acquired aplastic anemia characterized by a severe normocytic anemia with normal peripheral leukocyte and platelet counts, reticulocytopenia, high serum ferritin and transferrin saturation levels and isolated, almost complete absence of erythroblasts in the bone marrow with normal granulopoiesis and megakaryopoiesis. It presents with signs of severe anemia (fatigue, lethargy, pallor, intolerance of physical exercise and exertional dyspnea) in the absence of hemorrhagic symptoms.
Id765748009
StatusDefined
Associated morphologyaplasia
Finding sitestructuur van erytropoëtisch weefsel
Occurrencevolwassenheid
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD60.0
TermChronische verworven 'pure red cell aplasia'
SNOMED CT to Orphanet simple map98872
SNOMED CT to ICD-10 extended map
TargetD60.0
RuleTRUE
AdviceALWAYS D60.0
CorrelationSNOMED CT source code to target map code correlation not specified