progressieve nodulaire histiocytose (aandoening) | | progressieve nodulaire histiocytose | | Progressive nodular histiocytosis | | A rare normolipemic non-Langerhans cell histiocytosis characterized by progressive growth of multiple to disseminated asymptomatic skin lesions that range in appearance from yellow plaques to coalescence-prone red-brown papules, nodules and pedunculated tumors up to 5 cm in size, located typically on the face, trunk and extremities (and rarely on conjunctiva and mucous membranes). Characteristic microscopic findings include a storiform spindle cell infiltrate in the deep dermis with xanthoma macrophages and some Touton cells in the upper dermis. It is usually not associated with systemic disease. |
| Id | 765141005 | Status | Primitive |
DHD Diagnosethesaurus-referentieset |
referentieset met complexe 'mapping' naar ICD-10 | Target | D76.3 | Rule | TRUE | Advice | ALWAYS D76.3 | Correlation | SNOMED CT source code to target map code correlation not specified |
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