chronische huidziekte
non-Langerhans-cel-histiocytose
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progressieve nodulaire histiocytose (aandoening)
progressieve nodulaire histiocytose
Progressive nodular histiocytosis
A rare normolipemic non-Langerhans cell histiocytosis characterized by progressive growth of multiple to disseminated asymptomatic skin lesions that range in appearance from yellow plaques to coalescence-prone red-brown papules, nodules and pedunculated tumors up to 5 cm in size, located typically on the face, trunk and extremities (and rarely on conjunctiva and mucous membranes). Characteristic microscopic findings include a storiform spindle cell infiltrate in the deep dermis with xanthoma macrophages and some Touton cells in the upper dermis. It is usually not associated with systemic disease.
Id765141005
StatusPrimitive
Associated morphologyhistiocytaire proliferatie
Finding sitestructuur van dermis
Clinical courseprogressief
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD76.3
TermOverige histiocytosesyndromen
SNOMED CT to Orphanet simple map158022
SNOMED CT to ICD-10 extended map
TargetD76.3
RuleTRUE
AdviceALWAYS D76.3
CorrelationSNOMED CT source code to target map code correlation not specified