Progressive nodular histiocytosis (disorder)
Progressive nodular histiocytosis
A rare normolipemic non-Langerhans cell histiocytosis characterized by progressive growth of multiple to disseminated asymptomatic skin lesions that range in appearance from yellow plaques to coalescence-prone red-brown papules, nodules and pedunculated tumors up to 5 cm in size, located typically on the face, trunk and extremities (and rarely on conjunctiva and mucous membranes). Characteristic microscopic findings include a storiform spindle cell infiltrate in the deep dermis with xanthoma macrophages and some Touton cells in the upper dermis. It is usually not associated with systemic disease.
Associated morphologyhistiocytose - categorie
Finding sitestructuur van dermis
referentieset met complexe 'mapping' naar ICD-10
AdviceALWAYS D76.3
CorrelationSNOMED CT source code to target map code correlation not specified