| primair cutaan CD8-positief agressief epidermotroop cytotoxisch T-cellymfoom (aandoening) | | primair cutaan CD8-positief agressief epidermotroop cytotoxisch T-cellymfoom | | Berti-lymfoom
primair agressief CD8-positief epidermotroop cutaan T-cellymfoom
|  | Zeer zeldzaam huidlymfoom dat snel groeit; kan via het bloed uitzaaien naar andere delen van het lichaam, zoals de longen, teelballen, het zenuwstelsel, de lymfeklieren of de slijmvliezen van de mond. |  | Dit is een vorm van kanker in je huid. De kanker zit in de T-cellen die je lymfeklieren aanmaken. T-cellen helpen je lichaam om te vechten tegen infecties. | | Primary cutaneous CD8 positive aggressive epidermotropic cytotoxic T-cell lymphoma | | Primary cutaneous epidermotropic cytotoxic CD8 positive T-cell lymphoma
Berti lymphoma
| | Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma is a rare form of primary cutaneous T-cell lymphoma characterized by rapidly progressing, localized or disseminated nodules, tumors or eczematous skin lesions. It has a particularly aggressive clinical course with a high tendency to spread, in advanced stages, to extracutaneous locations (the central nervous system, lung, testes). Lymph nodes are often spared. |
| | DHD Diagnosis thesaurus reference set |
| SNOMED CT to Orphanet simple map | 178528 |
| SNOMED CT to ICD-10 extended map | | Target | C84.5 | | Rule | TRUE | | Advice | ALWAYS C84.5 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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