pseudoxanthoma elasticum-achtige papillaire dermale elastolyse (aandoening)
pseudoxanthoma elasticum-achtige papillaire dermale elastolyse
PXE-achtige papillaire dermale elastolyse
Pseudoxanthoma elasticum-like papillary dermal elastolysis
PXE-like (pseudoxanthoma elasticum-like) papillary dermal elastolysis
A rare acquired idiopathic dermal tissue disorder characterized by numerous asymptomatic 2-3 millimeter yellowish, non-follicular papules that tend to converge into cobblestone-like plaques. The plaques are distributed symmetrically over the posterior neck, supraclavicular region, axillae, and sometimes abdomen. Unlike pseudoxanthoma elasticum, these skin lesions show select elimination (absence or marked loss) of elastic fibers in the papillary dermis and there is no systemic involvement.
Associated morphologyafwijkend weefsel
Finding sitestructuur van huid
referentieset met complexe 'mapping' naar ICD-10
AdviceALWAYS Q82.8
CorrelationSNOMED CT source code to target map code correlation not specified