rabdomyosarcoom van cervix uteri (aandoening) | | rabdomyosarcoom van cervix uteri | | rabdomyosarcoom van baarmoederhals
| | Rhabdomyosarcoma of cervix uteri | | Cervical rhabdomyosarcoma
| | Rhabdomyosarcoma of the cervix uteri is a rare, highly malignant soft tissue sarcoma located in the uterine cervix and arising from primitive mesenchymal cells displaying skeletal muscle differentiation. It most often presents with abnormal vaginal discharge or dysfunctional uterine bleeding, abdominal pain and/or a cervical mass protruding into the vagina. Association with DICER1 syndrome has been reported. |
| DHD Diagnosis thesaurus reference set |
SNOMED CT to Orphanet simple map | 213802 |
SNOMED CT to ICD-10 extended map | Target | C53.9 | Rule | TRUE | Advice | ALWAYS C53.9 | MAPPED FOLLOWING WHO GUIDANCE | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | Correlation | SNOMED CT source code to target map code correlation not specified |
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