| idiopatische hypertrofische pachymeningitis (aandoening) | | idiopatische hypertrofische pachymeningitis |  | Dit betekent dat de vliezen die om je hersenen zitten, dikker zijn dan normaal. Er is geen duidelijke oorzaak. | | Immunoglobulin G4 related pachymeningitis | | IgG4-related pachymeningitis
Idiopathic hypertrophic pachymeningitis
| | A rare, brain inflammatory disease characterized by thickening of the dura mater of the cranium or spine with at least two histopathological features of IgG4-related disease: dense lymphoplasmacytic infiltrate, storiform fibrosis, and/or obliterative phlebitis. Patients typically have non-specific CSF findings and might be without systemic involvement or serum IgG4 elevation. Clinical manifestations are caused by mechanical compression of nerve or vascular structure, leading to functional deficit, most commonly headache, cranial nerve palsies, vision problems and motor weakness. |
| | PALGA thesaurus simple reference set for pathology |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | G03.9 | | Term | Meningitis, niet gespecificeerd |
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| SNOMED CT to Orphanet simple map | 449427 |
| SNOMED CT to ICD-10 extended map | | Target | G03.9 | | Rule | TRUE | | Advice | ALWAYS G03.9 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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