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primair maligne neuro-endocrien neoplasma van jejunum (aandoening)
primair maligne neuro-endocrien neoplasma van jejunum
primair maligne NEN van jejunum
Primary malignant neuroendocrine neoplasm of jejunum
Jejunal neuroendocrine tumor is a rare, primary, malignant, epithelial neoplasm of the small intestine arising from enterochromaffin cells in the jejunum. Clinical behavior depends on the histologic grade, but initially it is generally characterized by vague abdominal symptoms (cramping, bloating, diarrhea) with insidious onset, although sometimes it could present with signs of bowel obstruction/perforation or gastrointestinal bleeding. Diagnosis in advanced stages with regional or distant spread is common, but signs of carcinoid syndrome (flushing, sweating, diarrhea) are usually not apparent until hepatic metastasis has occurred.
Id737312002
StatusDefined
SNOMED CT to Orphanet simple map100077
SNOMED CT to ICD-10 extended map
TargetC17.1
RuleTRUE
AdviceALWAYS C17.1 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified
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