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verworven purpura fulminans (aandoening)
verworven purpura fulminans
Acquired purpura fulminans
A life-threatening, rapidly progressive thrombotic disorder affecting mainly neonates and children that is characterized by purpuric skin lesions and disseminated intravascular coagulation. It may progress rapidly to multi-organ failure caused by thrombotic occlusion of small and medium-sized blood vessels. There are two forms of the disorder that are classified according to triggering mechanisms: acute infectious (the most common form), and idiopathic purpura fulminans.
Id725157006
StatusDefined
Clinical courseacuut fulminant
Associated morphologynecrose
Finding sitestructuur van huid
Occurrencelevensperiode tussen geboorte en dood
Has interpretationafwijkend
Interpretshemostase
Associated morphologypurpura
Finding sitestructuur van huid
Occurrencelevensperiode tussen geboorte en dood
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD65
TermGedissemineerde intravasculaire stolling [defibrinatiesyndroom]
SNOMED CT to Orphanet simple map49566
SNOMED CT to ICD-10 extended map
TargetD65
RuleTRUE
AdviceALWAYS D65 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified