| hereditair 'peeling-skin'-syndroom (aandoening) | | hereditair 'peeling-skin'-syndroom | | erfelijk 'skin peeling'-syndroom
| | Hereditary skin peeling syndrome | | Familial continuous skin peeling syndrome
Peeling skin syndrome
| | A group of rare autosomal recessive forms of ichthyosis clinically characterized by superficial, asymptomatic, spontaneous peeling of the skin and histologically by a shedding of the outer layers of the epidermis. PSS presents with either an acral (acral PSS) or a generalized distribution for generalized PSS type A (noninflammatory) or B (inflammatory). |
| | Id | 724838009 | | Status | Primitive |
| DHD Diagnosis thesaurus reference set |
| SNOMED CT to Orphanet simple map | 817 |
| SNOMED CT to ICD-10 extended map | | Target | Q80.8 | | Rule | TRUE | | Advice | ALWAYS Q80.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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