congenitale afwijking van nier	congenitale afwijking van uterus	malformatiesyndroom met betrokkenheid van meerdere systemen
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syndroom van dubbele uterus, hemivagina en renale agenesie (aandoening)
	syndroom van dubbele uterus, hemivagina en renale agenesie
	syndroom van uterus didelphys, bicornis of bilocularis, geobstrueerde hemivagina en ipsilaterale nieragenesie OHVIRA-syndroom 'obstructed hemivagina and ipsilateral renal anomaly'-syndroom syndroom van Herlyn-Werner-Wunderlich HWW-syndroom Herlyn-Werner-Wunderlich-syndroom
	Double uterus, hemivagina, renal agenesis syndrome
	Double uterus and obstructed hemivagina syndrome Herlyn Werner syndrome Obstructed hemivagina and ipsilateral renal anomaly Wunderlich syndrome
	A rare congenital urogenital anomaly characterized by the presence of double uterus (didelphys, bicornuate or septum-complete or partial), unilateral cervico-vaginal obstruction and ipsilateral renal anomalies (renal agenesis and/or other urinary tract anomalies). Patients are usually diagnosed at puberty after menarche due to recurrent severe dysmenorrhea, chronic pelvic pain, excessive foul smelling mucopurulent discharge, spotting and intermenstrual bleeding (depending on the existence of uterine or vaginal communications). Fever, dyspareunia, and a palpable abdominal, pelvic or vaginal mass (mucocolpos or pyocolpos) may also be present.

Id	722431007
Status	Primitive

Associated morphology	morfologische afwijking
Finding site	structuur van nier
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

Associated morphology	morfologische afwijking
Finding site	structuur van uterus
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	Q51.1
Term	Verdubbeling van uterus met verdubbeling van cervix en vagina

Target	Q60.0
Term	Agenesie van nier, enkelzijdig

SNOMED CT to Orphanet simple map

3411

SNOMED CT to ICD-10 extended map

Target	Q51.1
Rule	TRUE
Advice	ALWAYS Q51.1 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified

Target	Q60.0
Rule	TRUE
Advice	ALWAYS Q60.0
Correlation	SNOMED CT source code to target map code correlation not specified