gonadale dysgenesie	malformatiesyndroom met betrokkenheid van meerdere systemen
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syndroom van hypoplasie van long, agonadisme, dextrocardie en hernia diaphragmatica (aandoening)
	syndroom van hypoplasie van long, agonadisme, dextrocardie en hernia diaphragmatica
	syndroom van pulmonale hypoplasie, agonadisme, dextrocardie en middenrifbreuk PAGOD-syndroom 'pulmonary hypoplasia, agonadism, omphalocele, dextrocardia, diaphragmatic hernia'-syndroom
	PAGOD syndrome
	PAGOD (pulmonary hypoplasia, hypoplasia pulmonary artery, agonadism, omphalocele, dextrocardia) syndrome Pulmonary hypoplasia, agonadism, dextrocardia, diaphragmatic hernia syndrome
	PAGOD syndrome is a severe developmental syndrome characterized by multiple congenital anomalies including cardiovascular defects, pulmonary hypoplasia, diaphragmatic defects and genital anomalies.

Id	722132007
Status	Primitive

Associated morphology	morfologische afwijking
Finding site	structuur van gonade
Occurrence	congenitaal
Pathological process	proces van pathologische ontwikkeling

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	Q87.8
Term	Overige gespecificeerde congenitale gestoorde-ontwikkelingssyndromen, niet elders geclassificeerd

SNOMED CT to Orphanet simple map

991

SNOMED CT to ICD-10 extended map

Target	Q87.8
Rule	TRUE
Advice	ALWAYS Q87.8 \| POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
Correlation	SNOMED CT source code to target map code correlation not specified