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Dianzani auto-immune lymfoproliferatieve ziekte (aandoening)
Dianzani auto-immune lymfoproliferatieve ziekte
Dianzani autoimmune lymphoproliferative disease
DALD
Dianzani autoimmune lymphoproliferative disease
DALD - Dianzani autoimmune lymphoproliferative disease
A very rare disorder with characteristics of autoimmunity, lymphadenopathy and/or splenomegaly. The prevalence is not known. The disorder has been reported in fewer than 30 patients to date. Age of onset is highly variable, ranging from childhood to young adulthood. A possible increased risk of cancer has been suggested in these patients. The cause is not known but it is thought to be hereditary. Biologically, DALD has characteristics of normal double-negative T-cells (DNTs) and defective in vitro FAS-mediated apoptosis. The pattern of inheritance of DALD is not known.
Id721093000
StatusPrimitive
Associated morphologylymfoproliferatieve aandoening
Pathological processauto-immuunproces
referentieset met complexe 'mapping' naar ICD-10
TargetD47.9
RuleTRUE
AdviceALWAYS D47.9 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified