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corticosteroïdesensitief aseptisch abces-syndroom (aandoening)
corticosteroïdesensitief aseptisch abces-syndroom
aseptische abcessen-syndroom
Corticosteroid sensitive aseptic abscess syndrome
A well-defined entity within the group of auto inflammatory disorders, it is a rare disease with 49 cases documented so far. It affects mainly young adults and is characterized by recurrent attacks of fever and deep abscess-like collections, most frequently localized in the abdomen. Aseptic abscesses may be either isolated or associated with an underlying condition such as relapsing polychondritis or inflammatory bowel disease. Antibiotics fail to cure the patients but dramatic improvements are seen with corticosteroids and immunosuppressive drugs.
Id720751000
StatusPrimitive
Associated morphologyabces
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetD89.8
TermOverige gespecificeerde aandoeningen waarbij immuunsysteem betrokken is, niet elders geclassificeerd
SNOMED CT to Orphanet simple map54251
SNOMED CT to ICD-10 extended map
TargetD89.8
RuleTRUE
AdviceALWAYS D89.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified