| corticosteroïdesensitief aseptisch abces-syndroom (aandoening) | | corticosteroïdesensitief aseptisch abces-syndroom | | aseptische abcessen-syndroom
| | Corticosteroid sensitive aseptic abscess syndrome | | A well-defined entity within the group of auto inflammatory disorders, it is a rare disease with 49 cases documented so far. It affects mainly young adults and is characterized by recurrent attacks of fever and deep abscess-like collections, most frequently localized in the abdomen. Aseptic abscesses may be either isolated or associated with an underlying condition such as relapsing polychondritis or inflammatory bowel disease. Antibiotics fail to cure the patients but dramatic improvements are seen with corticosteroids and immunosuppressive drugs. |
| | Id | 720751000 | | Status | Primitive |
| Associated morphology | abces |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | D89.8 | | Term | Overige gespecificeerde aandoeningen waarbij immuunsysteem betrokken is, niet elders geclassificeerd |
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| SNOMED CT to Orphanet simple map | 54251 |
| SNOMED CT to ICD-10 extended map | | Target | D89.8 | | Rule | TRUE | | Advice | ALWAYS D89.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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