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congenitale analbuminemie (aandoening)
congenitale analbuminemie
Congenital analbuminemia
Congenital analbuminemia (CAA) is characterized by the absence or dramatic reduction of circulating human serum albumin (HSA).
Id718721006
StatusPrimitive
Occurrencecongenitaal
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetE88.0
TermStofwisselingsstoornissen van plasmaproteïne, niet elders geclassificeerd
SNOMED CT to Orphanet simple map86816
SNOMED CT to ICD-10 extended map
TargetR77.0
RuleTRUE
AdviceALWAYS R77.0
CorrelationSNOMED CT source code to target map code correlation not specified