teleangiëctasie van huid
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cutane collageneuze vasculopathie (aandoening)
cutane collageneuze vasculopathie
cutaneous collagenous vasculopathy
CCV
Cutaneous collagenous vasculopathy
A primary microangiopathy confined to the skin with characteristics of multiple and widespread telangiectasia. It is a rare disorder with less than 20 cases reported in the literature to date. Most patients present in adulthood with symmetrical telangiectasia appearing on the lower extremities and later progressing to the trunk and upper extremities. Thought to be associated with collagen abnormalities in the skin microvasculature.
Id718634003
StatusPrimitive
Associated morphologygegeneraliseerde teleangiëctasieën
Finding sitestructuur van microscopische huidvasculatuur
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetI78.1
TermNiet-neoplastische naevus
SNOMED CT to Orphanet simple map280779
SNOMED CT to ICD-10 extended map
TargetI78.1
RuleTRUE
AdviceALWAYS I78.1
CorrelationSNOMED CT source code to target map code correlation not specified