Graham-Little-Piccardi-Lassueur-syndroom (aandoening)
syndroom van Graham-Little-Piccardi-Lassueur
syndroom van Graham-Little
Graham Little Piccardi Lassueur syndrome
Graham Little syndrome
Piccardi Lassueur Little syndrome
A variant of lichen planopilaris characterized by the clinical triad of progressive cicatricial (scarring) alopecia of the scalp, follicular keratotic papules on glabrous skin, and variable alopecia of the axillae and groin. It is a very rare disease but the exact prevalence is not known. It mainly affects women during adulthood (30-60 years of age). Scarring alopecia presents as small confluent patches that are atrophic and cicatricial in the center but erythematous and squamous around the edges. Follicular keratosis presents as pruritic, red-brown, follicular spiny papules on the trunk and extremities. Generally, the three clinical features appear simultaneously but in some cases, scalp alopecia precedes the follicular keratosis. Etiology is unknown.
Associated morphologylichenificatie
Finding sitestructuur van huid
Associated morphologypapuleus exantheem
Finding sitestructuur van huid
Associated morphologyinflammatoire morfologie
Finding sitestructuur van huid
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TermLichen planopilaris
SNOMED CT to Orphanet simple map505
SNOMED CT to ICD-10 extended map
AdviceALWAYS L66.1
CorrelationSNOMED CT source code to target map code correlation not specified