| | primair pulmonaal lymfoom (aandoening) |  |  | primair pulmonaal lymfoom |  |  | Primary pulmonary lymphoma |  |  | A rare neoplastic disease defined as a clonal lymphoid proliferation affecting one or both lungs (parenchyma and/or bronchi) in a patient with no detectable extrapulmonary involvement at diagnosis or during the subsequent 3 months. PPL comprises low grade/indolent B cell PPL forms, the most frequent form represented by the marginal B-cell lymphoma of mucosa associated lymphoid tissue (MALT lymphoma) and other non-MALT low grade lymphomas; and more rarely high-grade B-cell PPL (including diffuse large B cell lymphoma) and lymphomatoid granulomatosis (LYG). | 
 | | Id | 718200007 |  | Status | Primitive | 
| DHD Diagnosis thesaurus reference set | 
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set |  | | Target | C85.7 |  | Term | Overige gespecificeerde typen van non-Hodgkin-lymfoom | 
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| SNOMED CT to Orphanet simple map | 2420 | 
| SNOMED CT to ICD-10 extended map |  | | Target | C85.7 |  | Rule | TRUE |  | Advice | ALWAYS C85.7 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE |  | Correlation | SNOMED CT source code to target map code correlation not specified | 
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