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Non-amyloid fibrillary glomerulonephritis (disorder)
Non-amyloid fibrillary glomerulonephritis
Congo red negative amyloidosis like glomerulopathy
Non-amyloid fibrillary glomerulopathy
Non-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy are often grouped together as pathogenetically related diseases.
Id718192000
StatusPrimitive
Associated morphologyinflammatoire morfologie
Finding sitestructuur van glomerulus
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetN03.6
TermChronisch nefritisch syndroom; Dense deposit disease
SNOMED CT to Orphanet simple map97566
SNOMED CT to ICD-10 extended map
TargetN03.6
RuleTRUE
AdviceALWAYS N03.6 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified