Non-amyloid fibrillary glomerulonephritis (disorder) | | Non-amyloid fibrillary glomerulonephritis | | Congo red negative amyloidosis like glomerulopathy Non-amyloid fibrillary glomerulopathy
| | Non-amyloid fibrillary glomerulopathy (non-amyloid FGP) is a rare cause of glomerulonephritis (GN) characterized by glomerular accumulation of non-amyloid fibrils in the mesangium and the glomerular (and rarely tubular) basement membrane, that mainly presents with renal insufficiency, micro-hematuria and nephrotic range proteinuria. Non-amyloid FGP and immunotactoid glomerulopathy are often grouped together as pathogenetically related diseases. |
| Id | 718192000 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | Target | N03.6 | Term | Chronisch nefritisch syndroom; Dense deposit disease |
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SNOMED CT to Orphanet simple map | 97566 |
SNOMED CT to ICD-10 extended map | Target | N03.6 | Rule | TRUE | Advice | ALWAYS N03.6 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | Correlation | SNOMED CT source code to target map code correlation not specified |
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