primaire gelokaliseerde cutane amyloïdose
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primaire gelokaliseerde nodulaire cutane amyloïdose (aandoening)
primaire gelokaliseerde nodulaire cutane amyloïdose
Dit betekent dat je kleine, harde knobbeltjes op je huid hebt. De knobbeltjes komen doordat eiwitten zich ophopen. Eiwitten zijn belangrijke bouwstoffen. Je lichaam heeft eiwitten nodig voor groei en herstel.
Primary localized cutaneous nodular amyloidosis
Nodular amyloidosis
PLCNA - Primary localized cutaneous nodular amyloidosis
Primary localized cutaneous nodular amyloidosis (PLCNA) is the most rare form of primary cutaneous amyloidosis, a skin disease characterized by the accumulation of amyloid deposits in the dermis, characterized clinically by yellowish waxy crusted nodules and papules on the face, lower extremities, trunk, scalp, and genitalia and histologically by the localized deposition of immunoglobulin-derived amyloid in the papillary dermis and subcutis. PLCNA can be associated with connective tissue disorders such as Sjögren's syndrome and CREST syndrome.
Id716704007
StatusPrimitive
Associated morphologyfocaal amyloïd
Finding sitestructuur van huid
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetE85.4
TermAmyloïdose beperkt tot orgaan
SNOMED CT to Orphanet simple map137810
SNOMED CT to ICD-10 extended map
TargetE85.4
RuleTRUE
AdviceALWAYS E85.4
CorrelationSNOMED CT source code to target map code correlation not specified
TargetL99.0
RuleTRUE
AdviceALWAYS L99.0 | THIS CODE MAY BE USED IN THE PRIMARY POSITION WHEN THE MANIFESTATION IS THE PRIMARY FOCUS OF CARE
CorrelationSNOMED CT source code to target map code correlation not specified