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immuungemedieerde necrotiserende myopathie (aandoening)
immuungemedieerde necrotiserende myopathie
INM
auto-immune necrotiserende myopathie
IMNM
Autoimmune necrotizing myopathy
Immune mediated necrotizing myopathy
A rare form of idiopathic inflammatory myopathy characterized by acute or subacute, severe, symmetrical, proximal muscle weakness usually associated with muscle-specific antibodies (anti-HMGCR or anti-SRP). Histopathological characteristics include myocyte necrosis and regeneration without significant inflammation, and C5b-9 deposition on non-necrotic myofibers.
Id715863001
StatusDefined
Associated morphologynecrotiserende ontsteking
Finding sitestructuur van skeletspier
Pathological processauto-immuunproces
PALGA thesaurus simple reference set for pathology
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetG72.4
TermInflammatoire myopathie, niet elders geclassificeerd
SNOMED CT to Orphanet simple map206569
SNOMED CT to ICD-10 extended map
TargetG72.4
RuleTRUE
AdviceALWAYS G72.4
CorrelationSNOMED CT source code to target map code correlation not specified