immuungemedieerde necrotiserende myopathie (aandoening)
immuungemedieerde necrotiserende myopathie
auto-immune necrotiserende myopathie
Autoimmune necrotizing myopathy
Immune mediated necrotizing myopathy
A rare form of idiopathic inflammatory myopathy with clinical manifestation of acute or subacute proximal muscle weakness and histopathological features of myocyte necrosis and regeneration without significant inflammation. The main presenting feature is subacute severe symmetrical proximal myopathy with a markedly elevated creatine kinase level. The course is often severe but may be self-limiting and recovery may occur within weeks to months of discontinuing the causative agent, if identified. The disease is thought to be related to an immune response possibly triggered by drug therapy, connective tissue diseases, or cancer. The exact mechanism underling the disorder is not known but some autoantibodies appear to be a likely cause. Malignancy may be involved.
Associated morphologynecrotiserende ontsteking
Finding sitestructuur van skeletspier
Pathological processauto-immuunproces
PALGA thesaurus simple reference set for pathology
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TermInflammatoire myopathie, niet elders geclassificeerd
SNOMED CT to Orphanet simple map206569
SNOMED CT to ICD-10 extended map
AdviceALWAYS G72.4
CorrelationSNOMED CT source code to target map code correlation not specified