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neuronale intranucleaire inclusieziekte (aandoening)
neuronale intranucleaire inclusieziekte
Neuronal intranuclear inclusion disease
Neuronal intranuclear inclusion disease (NIID) is a very rare multisystem neurodegenerative disorder characterized by the presence of eosinophilic intranuclear inclusions in neuronal and glial cells, and neuronal loss.
Id715437003
StatusPrimitive
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetG31.0
TermCircumscripte hersenatrofie
SNOMED CT to Orphanet simple map2289
SNOMED CT to ICD-10 extended map
TargetG31.0
RuleTRUE
AdviceALWAYS G31.0 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified